Congenital facial paralysis - presentation of a clinical case
Keywords:
Congenital facial paralysis, Moebius syndromeAbstract
Congenital facial paralysis is presented clinically as decreased or absent movement of the facial muscles, which is found at birth and is due to impaired or completely missing function of the facial nerve. Etiology for disease includes two major groups -intrapartum injury or various developmental disorders.
Facial nerve aplasia is an extremely rare anomaly that usually occurs in association with Moebius syndrome. Moebius syndrome is a rare neurological disorder characterized by weakness or paralysis (palsy) of multiple cranial nerves, most often the 6th (abducens) and 7th (facial) nerves, resulting in limitation of lateral gaze movement and facial diplegia. We present a case of an 8-year-old girl with probable hypoplasia of the nuclei of the facial nerves and the nuclei of nn abducens.
Although aplasia or hypoplasia of the facial nerve is rare, their recognition is clinically important for its prognostic and medicolegal implications.
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Copyright (c) 2021 Asia Asenova, I. Aleksandrova, A. Shokova, E. Rodopska, N. Topalov, V. Bojinova
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